β£What is constriction ring syndrome?aka Amniotic band syndrome, Streeter's Dysplasiaβ£What is the inheritance?Sporadic and non hereditaryUnkown causeβ£Clinical features of constriction band syndrome?Bands perpendicular to digitProximal to band, limb is normalβ£Associated deformities with constriction band syndrome?ClubfootLLDSyndactylyβ£Classification of constriction band syndrome?Patterson Classification - presence of deformityType 1 = simple - no deformity2 = deformity / lymphedema distal to ring e.g. hypoplasia, lymphedema3 = fusions distally (syndactyly)4 = intrauterine amputationβ£What is the management of constriction ring syndrome?Goal is to improve function and cosmesisType 1 = can release bandsβ£Type 2 = Circumferential Z-plasties OR direct closure also describedOne stage vs 2 stagedRecommended 2 stage if circumferential to prevent problems with distal circulationFirst stage, release one half of circumference. Edema should resolve in few weeks3-6 months later, release other halfType 3 = address syndactyly